Mieloma osteosclerótico (síndrome poems). Presentación de un caso. Osteosclerotic Myeloma- POEMS syndrome: A case report
Abstract
Se presentó el caso de una paciente de 42 años de edad, raza blanca, que presentó hiperpigmentación dérmica en cara, cuello y parte superior del tórax, decaimiento, cefalea occipital y pérdida de peso, posteriormente le aparecen manchas blanquecinas en las zonas hiperpigmentadas que le producen prurito y ardentía intensa. En los estudios que se le realizaron la eritrosedimentación siempre tuvo cifras elevadas, se informó una marcada agrupación eritrocitaria y hepatomegalia ligera, en las dos biopsias de piel que se le hicieron no se concluyó diagnóstico, el informe de la biopsia de médula ósea fue: infiltrado intersticial por células plasmáticas maduras e inmaduras, marcada osteosclerosis, compatible con un mieloma osteosclerótico. En los días que se esperaba el resultado de este estudio inició un síndrome febril agudo acompañado de sudoración, falta de aire intensa y fallece.
Palabras clave: ERITROSEDIMENTECIÓN ELEVADA, MIELOMA OSTEOSCLERÓTICO.
ABSTRACT
A 42 year old Caucasian female patient presented dermic hyperpigmentation in face, neck and upper thoracic part. Depression, occipital headache and weight loss were other presenting symptoms; some whitish spots appeared in those hyperpigmented zones producing itch and burning pain. Erytrosedimentation tests always had augmented level a marked erythrocyte aggregation and mild hepatomegaly were observed. Diagnosis was not concluded in two skin biopsies performed. The report of bone marrow biopsy was: interstitial infiltration by mature and immature plasmatic cells a marked osteosclerosis associated with osteosclerotic myeloma. While expecting for the results of this study an acute fevered syndrome and sweating and severe dyspnea appeared and the patient died.
Key words: BLOOD SEDIMENTATION, OSTEOSCLEROTIC MYELOMA.
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