Embryonic vaginal rhabdomyosarcoma

Authors

  • Tania Pampillo Castiñeiras Hospital Pediátrico Provincial Pepe Portilla. Pinar del Río. Cuba.
  • Lourdes Milagros Reyes Puentes Hospital Pediátrico Provincial Docente “Pepe Portilla”. Pinar del Río.
  • Vladimir Díaz Noda Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.
  • Agustín Lemus Saraceni Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.
  • Ricelo Sierra Herrera Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.

Keywords:

RHABDOMYOSARCOMA, EMBRYONAL, VAGINAL NEOPLASMS, PEDIATRICS

Abstract

Introduction: rhabdomyosarcoma is a malignant tumor of soft tissues, of embryonal, mesenchymal origin, and constitutes 50% of soft tissue sarcomas and 4 to 8% of solid tumors in children. Histologically, it resembles the striated muscles of the fetus. It can originate in the head, neck and genitourinary system. Its etiology includes genetic anomalies and toxic consumption. There are four histological subtypes: embryonal, alveolar, botryoidal and pleomorphic; however, there is complexity to the diagnosis of an entity as infrequent as a tumor of embryonal origin in a little girl.

 

Objective: to report the case of a vaginal sarcoma suspected by ultrasound, in a little girl with genitorrhagia.


Case report: the main symptom was genital bleeding in a one-year-old patient. The initial physical examination was negative, the first ultrasound detected an echogenic image at the hypogastric level, rounded, well-delimited, irregular, heterogeneous , with a diameter greater than 26 mm, without calcifications, dependent on internal genitalia, an exploratory laparotomy was performed that corroborates the echographic diagnosis, the evolution was satisfactory.

Conclusion: despite its rarity and complexity, it is possible to perform the ultrasound diagnosis of a vaginal sarcoma satisfactorily in a small girl with genitorrhagia.

 

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Author Biographies

Tania Pampillo Castiñeiras, Hospital Pediátrico Provincial Pepe Portilla. Pinar del Río. Cuba.

Médica. Especialista de Segundo Grado en Pediatría. Máster en Atención Integral al Niño y en Procederes Diagnósticos en Atención Primaria de Salud. Profesor Auxiliar.

Lourdes Milagros Reyes Puentes, Hospital Pediátrico Provincial Docente “Pepe Portilla”. Pinar del Río.

Master en Atención Integral al niño y en Procederes Diagnósticos en APS. Especialista de Primer y Segundo Grado en Pediatría. Auxiliar. Dirección:

Vladimir Díaz Noda, Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.

Médico. Especialista de Segundo Grado en Ginecología y Obstetricia. Máster en Atención Integral a la Mujer. Profesor Auxiliar.

Agustín Lemus Saraceni, Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.

Médico.Especialista de Segundo Grado en Anatomía Patológica. Máster en Atención Integral al Adulto Mayor. Profesor Auxiliar.

Ricelo Sierra Herrera, Hospital General Docente Abel Santamaría Cuadrado. Pinar del Río. Cuba.

Médico. Especialista de Segundo Grado en Ginecología y Obstetricia. Másteren Atención Integral a la Mujer. Profesor Auxiliar.

References

1- Olarte P, Duarte R, Lora A. Rabdomiosarcoma retroperitoneal en el adulto. Rev Colomb Cir [Internet]. 2012 Sep [citado 2016 Mar 23]; 27(3): 235-41. Disponible en: http://www.scielo.org.co/pdf/rcci/v27n3/v27n3a9.pdf

2- Morante Valverde R, Cabezalí Barbanco D, Moreno Zegarra C, González Herrero M, Tordable Ojeda C, López Vázquez F, et al. Rabdomiosarcoma genitourinario en la infancia, nuestra experiencia. Cir Pediatr [Internet]. 2014 Oct [citado 2017 Jun 5]; 27(2):[aprox. 5 p.]. Disponible en: https://www.secipe.org/coldata/upload/revista/2014_27-2_53-56.pdf

3- Dumont SN, Araujo DM, Munsell MF, Salganick JA, Dumont AG, Raimond KA, et al. Management and outcome of 239 adolescent and adult rhabdomyosarcoma patients. Cancer Med [Internet]. 2013 [cited 2016 Oct 11];2(4): [about 12 p.]. Disponible en: http://onlinelibrary.wiley.com/doi/10.1002/cam4.92/full.

4- MINSAP. Dirección Nacional de Registros Médicos y Estadísticas de Salud. Anuario Estadístico de Salud 2016 [Internet]. 2017 [Citado 2017 Feb 27]. Disponible en: http://files.sld.cu/dne/files/2017/05/Anuario_Estad%C3%ADstico_de_Salud_e_2016_edici%C3%B3n_2017.pdf

5-Khosla D, Sapkota S, Kapoor R, Kumar R, Sharma SC. Adult rhabdomyosarcoma: Clinical presentation, treatment, and outcome. J Can Res Ther [Internet]. 2015 [citado 2017 Jul 11];11 (4): 830-4. Disponible en: http://www.cancerjournal.net/article.asp?issn=0973-1482;year=2015;volume=11;issue=4;spage=830;epage=834;aulast=Khosla

6- Instituto Nacional del Cáncer. Tratamiento del sarcoma de tejido blando en adultos [Internet]. 2017 Jun [citado 2017 junio 5]. Disponible en: https://www.cancer.gov/espanol/tipos/sarcoma-de-tejido-blando/pro/tratamiento-tejido-blando-adultos-pdq

7- Martín Zaya A, González AC, Sandrone SS, Sambueli Ruben H. Sarcoma de células foliculares dendríticas de vagina en paciente con carcinoma de vías urinarias. A propósito de un caso. Revista de la Facultad de Ciencias Médicas (Córdova) [Internet]. 2016 Jun [citado 2017 junio 5]; 73 (2): 126-31. Disponible en: https://revistas.unc.edu.ar/index.php/med/article/view/13246

8- Chakrabarty SB, Sarkar A, Ray J, Tigga MP. Sarcoma botryoides in a 14 year old girl: a rare case. Int J Reprod Contracept Obstet Gynecol [Internet]. 2015 [citado 2016 Oct 11]; 4(3): 923-9. Disponible en: http://www.scopemed.org/?jft=89&ft=89-doi:10.18203/2320-1770.ijrcog20150132

9-Sandoval Diaz I, Hernández Alarcón R, Torres Arones E. Mioma cervical gigante en adolescente. Rev Chil Obstet Ginecol [Internet]. 2015 Ago [citado 2016 Oct 11]; 80(4): 337-40. Disponible en: http://www.scielo.cl/pdf/rchog/v80n4/art09.pdf

10-Vega Betancourt N, Jiménez Puñales S, Rodríguez Santos IC. Rabdomiosarcoma botrioide del aparato genital femenino en paciente adolescente virgen. Rev Cubana Obstet Ginecol [Internet]. 2016 Dic [citado 2017 Jul 11];42(4): 524-9. Disponible en: http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0138-600X2016000400012

11-dos Santos Benedetti GM, Garanhani ML, Aparecida Sales C. El tratamiento de cáncer infantil-juvenil: revelando las experiencias de los padres. Rev Latino Am Enfermagem [Internet]. 2014 May-Jun [citado 2016 Oct 11]; 22(3): 425-31 Disponible en: http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0104-11692014000300425&lng=en

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Published

2017-12-28

How to Cite

1.
Pampillo Castiñeiras T, Reyes Puentes LM, Díaz Noda V, Lemus Saraceni A, Sierra Herrera R. Embryonic vaginal rhabdomyosarcoma. Rev Ciencias Médicas [Internet]. 2017 Dec. 28 [cited 2025 Sep. 17];22(1):198-204. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/3361

Issue

Vol. 22 No. 1 (2018)

Section

CASE REPORTS

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