Juvenile Sjögren’s syndrome with a presentation of renal distal tubular acidosis

Authors

Keywords:

SJOGREN'S SYNDROME, ACIDOSIS, RENAL TUBULAR, LYMPHOCYTES, EXOCRINE GLANDS, PATIENT.

Abstract

Introduction: the Syndrome of Sjögren is an exocrinopatía autoinmune characterized by an infiltrated inflammatory, with linfocitos prevalence in glands exocrinas and knitted extraglandulares. The glandular lesion is characterized by the hiposecreción in mucous oral and ocular. 

Clinical case: a 13-year-old female adolescent with Sjögren's Syndrome is presented, whose initial clinical manifestation was extra-glandular, with the kidney as the main affected organ in type-I distal renal tubular acidosis.

Conclusions: it is demonstrated that the realization of a meticulous anamnesis, clinical exploration and the use of different diagnostic tools, they make possible a precocious diagnosis of the illness and of their manifestations extraglandulares. 

 

Downloads

Download data is not yet available.

Author Biographies

Didier Rodríguez Matanzas, Hospital Clínico Quirúrgico Docente León Cuervo Rubio

Especialista 1er Grado en Reumatologia

Yanet Cruz García, Hospital Clínico Quirúrgico Docente León Cuervo Rubio

Dra. Ms, Especialista en 1er Grado MGI, Especialista en 1er Grado Reumatología

References

1. Canteras DT, Alonso A, Enfermedad mixta del tejido conectivo, síndromes de superposición, síndrome de Sjögren, In: Coto C, Reumatología pediátrica. 2012. p 259-263. http://www.bvs.sld.cu/libros/reumatologia_pediatrica/cap18.pdf

2. Corominas H, Fíguls R y Riera M. Síndrome de Sjögren. Reumatol Clin. [Internet]. 2008 [citado 4/11/2020]; 4(supl1): s22-7. https://www.reumatologiaclinica.org/es-pdf-S1699258X08761357

3. Gómez M del P, Rojas JP. Síndrome de Sjögren en pediatría: diagnóstico y manejo. Rev. Colomb. Reumatol. [Internet]. Dic. 2012 [citado 4/11/2020]; 19(4): 245-250. https://www.elsevier.es/es-revista-revista-colombiana-reumatologia-374-pdf-S0121812312700191

4. Ríos Gomes Bica BE, Saldarriaga Rivera LM, de Almeida Tupinambá H, Leitão de Azevedo MN. Síndrome de Sjögren juvenil primario: Estudio de cohorte. Rev cubana de Reumatolo [Internet]. 2015 [citado 4/11/2020]; 17(1): [aprox. 7 p.]. Disponible en: http://www.revreumatologia.sld.cu/index.php/reumatologia/article/view/384

5. Polanco NA, Soto MV y Rodríguez F, Síndrome de Sjögren y acidosis tubular renal distal reversible: una mirada a sus manifestaciones renales.Rev. Colomb Reumatol. [Internet]. Dic. 2013 [citado 4/11/2020] 2013; 20(4): 250-254 https://www.elsevier.es/es-revista-revista-colombiana-reumatologia-374-pdf-S0121812313701397

6. Méndez D. Acidosis tubular renal asociado a Síndrome de Sjögren primario. Rev Clín Esc Med [Internet]. Dic. 2019 [citado 4/11/2020]; 9(5): 45-49. https://www.medigraphic.com/cgi-bin/new/resumen.cgi?IDARTICULO=90301

7. Sarma A. Hypokalemic paralysis due to primary Sjögren syndrome. Indian J Endocr Metab. [Internet]. 2018 [citado 4/11/2020]; 22(2):287-289. https://www.ijem.in/article.asp?issn=2230-8210;year=2018;volume=22;issue=2;spage=287;epage=289;aulast=Sarma

8. Riega Torres JCL, et al. Síndrome de Sjögren(SS), revisión del tema y saliva como método diagnóstico. Gac Med Mex. 2016[Internet]. 2016 [citado 4/11/2020]; 152: 371-80 https://www.anmm.org.mx/GMM/2016/n3/GMM_152_2016_3_371-380.pdf

9. Jung SW, Park EJ, Kim JS et al. Renal tubular acidosis in patients with primary Sjögren’s syndrome. Electrolyte Blood Press [Internet]. 2017 [citado 4/11/2020]; 15(1):17-22. https://pubmed.ncbi.nlm.nih.gov/29042903/

10. Kassan SS, Moutsopoulos HM, Moutsopoulos MD. Clinical manifestations and early diagnosis of Sjögren Syndrome. Arch Intern Med. 2004[Internet]. 2004 [citado 4/11/2020]; 164 (12): 1275-1284. https://jamanetwork.com/journals/jamainternalmedicine/article-abstract/217138

Downloads

Published

2021-03-05

How to Cite

1.
Rodríguez Matanzas D, Cruz García Y, Urquiaga Rosa JR. Juvenile Sjögren’s syndrome with a presentation of renal distal tubular acidosis. Rev Ciencias Médicas [Internet]. 2021 Mar. 5 [cited 2025 Oct. 10];25(2):e4743. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/4743

Issue

Vol. 25 No. 2 (2021)

Section

CASE REPORTS

License

Authors who have publications with this journal agree to the following terms: Authors will retain their copyrights and grant the journal the right of first publication of their work, which will be publication of their work, which will be simultaneously subject to the Creative Commons Attribution License (CC-BY-NC 4.0) that allows third parties to share the work as long as its author and first publication in this journal are indicated.

Authors may adopt other non-exclusive license agreements for distribution of the published version of the work (e.g.: deposit it in an institutional telematic archive or publish it in a volume). Likewise, and according to the recommendations of the Medical Sciences Editorial (ECIMED), authors must declare in each article their contribution according to the CRediT taxonomy (contributor roles). This taxonomy includes 14 roles, which can be used to represent the tasks typically performed by contributors in scientific academic production. It should be consulted in monograph) whenever initial publication in this journal is indicated. Authors are allowed and encouraged to disseminate their work through the Internet (e.g., in institutional telematic archives or on their web page) before and during the submission process, which may produce interesting exchanges and increase citations of the published work. (See The effect of open access). https://casrai.org/credit/