Diagnostic and therapeutic considerations on Brudaga syndrome

Authors

Keywords:

BRUGADA SYNDROME, ELECTROCARDIOGRAPHY, DEATH, SUDDEN, CARDIAC, GENETICS.

Abstract

Introduction: brudaga syndrome is an inherited cardiac condition characterized by abnormal electrocardiogram (ECG) patterns. It was initially described in 1992 by the Brugada brothers and is associated with an increased risk of sudden cardiac death. Objective: to analyze the current diagnostic and therapeutic advances in Brudaga syndrome. Methods: analysis of original articles and bibliographic reviews previously carried out that provided information on the advances in the diagnosis of Brudaga Syndrome, in addition, the search for information in different databases such as Scielo, Elsevier, PubMed, Chrocane, Epistemonikos, and different journals including Seimic, Medigraphic Artemis, Recimundo, SCIENCE, MEDICRIT was prioritized.

Development: diagnosis is based on the identification of specific patterns in the ECG, being crucial to recognize the Brugada type 1 pattern, which shows a pronounced ST-segment elevation in certain leads. Symptoms may vary and include fainting, arrhythmias and, in severe cases, sudden cardiac death. Management of Brugada syndrome may involve the placement of implantable cardioverter defibrillators and the use of certain drugs, such as quinidine. Genetic counseling is essential, especially to identify relatives at risk. In addition, known triggers, such as certain drugs and substances, should be avoided.

Conclusions: the correct interpretation of the electrocardiogram plays a crucial role in the diagnosis of Brugada syndrome. However, it is imperative to complement this analysis with a thorough clinical evaluation, considering family history and present symptoms.

 

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References

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Published

2025-04-30

How to Cite

1.
López-Barrionuevo CG, Enrriquez-Grijalva MF, Reascos-Chalacán MY. Diagnostic and therapeutic considerations on Brudaga syndrome. Rev Ciencias Médicas [Internet]. 2025 Apr. 30 [cited 2025 Sep. 19];29(1):e6746. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/6746

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Vol. 29 No. 1 (2025): Publicación Continua

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