Neurofibromatosis type-I involving the upper maxilla
Keywords:
Neurofibromatosis 1, Mouth diseases.Abstract
ABSTRACT OK
Introduction: Von Recklinghausen disease or neurofibromatosis type I (NF1) is an autosomal dominant disease with a wide clinical expression, with manifestations ranging from multiple café-au-lait spots to severe functional and aesthetic complications affecting bone tissue and nerve. Oral manifestations of NF1 are rare, affecting some patients.
Case report: a case presenting neurofibromatous lesions in the upper alveolar ridge, maxillary tuberosity and part of the pterygomaxillary cavity, indicating surgical excision due to the difficulties presented when using dental prosthesis and the risk of trauma for this tumor during the mastication process. The relevance of this research lies in the fact that the disease rarely occurs in oral cavity. The size of the tumor, the surgical approach applied and the functional and aesthetic results obtained are shown, with no evidence of recurrence to date.
Conclusions: a case of neurofibromatosis was presented, located in the alveolar ridge, maxillary tuberosity and pterygomaxillary cavity. Treatment made possible the functional and aesthetic rehabilitation of the patient.
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