Disseminated Superficial Actinic Porokeratosis

Authors

  • Adialys Acosta Rodríguez Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.
  • Javier Martinez Navarro Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.
  • Elizabeth Fernández López Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.

Keywords:

POROKERATOSIS, GENETIC SKIN DISEASES, DERMATOLOGY.

Abstract

Introduction: porokeratosis is a hereditary disorder of keratinization. Multiple clinical variants are described, all represented by a common primary lesion: the hyperkeratotic papule. The diagnosis is confirmed with histopathological study, where the cornoid lamella is appreciated, the most representative finding in this dermatosis. The poor response to therapy, the frequent recurrence and its potential preneoplastic nature, make this pathology a complex problem for the dermatologists. One of its variants, the disseminated superficial actinic porokeratosis, is the most frequent clinical form with onset in the third and fourth decades of life, affecting with little predominance the female sex.

Objective: to present a case with disseminated superficial actinic porokeratosis (DSAP) confirmed by cutaneous biopsy in a 30-year-old woman.

Case report: a woman who comes to the Dermatology Office presenting skin lesions accompanied by intense pruritus located in the upper and lower limbs, mainly in the areas exposed to sunlight, of 2 years of evolution. In the medical interview, it was found that the mother presented the similar skin lesions in photo-exposed areas, whose pathological diagnosis was disseminated superficial actinic porokeratosis. The dermatological physical examination allows suspecting this entity, which is confirmed by biopsy.

Conclusions: even though this is a rare entity, the diagnosis can be clinically made considering the symptoms, family history, dermatological physical examination, and the confirmation by means of skin biopsy.

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Author Biographies

Adialys Acosta Rodríguez, Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.

Especialista de Primer Grado en Dermatología. Instructora.

Javier Martinez Navarro, Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.

Especialista de Primer Grado en Anatomía Patológica.

Elizabeth Fernández López, Hospital General Universitario Dr. Gustavo Aldereguía Lima. Cienfuegos.

Especialista de Primer Grado en Dermatología. Profesora Asistente.

References

1. Sánchez Galbán L, Díaz Leonard D, Betancourt Trujillo M. Poroqueratosis. Presentación de un caso. Medisur [Internet]. 2017 [citado 10 Nov 2017]; 15(4): [aprox. 5 p.]. Disponible en: http://www.medisur.sld.cu/index.php/medisur/article/view/3465/2356.

2. Cabrera HN, Mohr YA, Sánchez G. Poroqueratosis genitoglútea: una rara enfermedad habitualmente mal diagnosticada. Dermatol Argent [Internet]. 2015 [citado 10 Nov 2017]; 21 (3): 220-223 [aprox. 3 p.]. Disponible en: http://dermatolarg.org.ar/index.php/dermatolarg/article/viewFile/1423/813

3. Aquino Farrera CJ, López Vázquez F, García Gil A, Toussaint Care S, Lacy Niebla RM. Poroqueratosis superficial diseminada no actínica en una paciente con miocardiopatía dilatada. Dermatol Rev Mex [Internet] 2015[citado 10 Nov 2017]; 59: [aprox. 5 p.]. Disponible en: http://www.medigraphic.com/pdfs/derrevmex/rmd-2015/rmd156j.pdf.

4. Valiente Rebull C, Rodríguez L, Martínez Braga G, Di Martino Ortiz B, Rodríguez Masi M, et al. Poroqueratosis. Reporte de tres casos. Our Dermatol Online [Internet] 2014[citado 10 Nov 2017]; 5(2): [aprox. 5 p.]. Disponible en: http://www.odermatol.com/odermatology/22014/14.Porokeratosis-ValienteRebullC.pdf

5. Bordel MT, Martínez G, Miranda A. Poroqueratosis actínica superficial diseminada asociada a linfedema crónico primario. Actas Dermosifiliogr [Internet] 2004 [citado 10 Nov 2017]; 95(2): [aprox. 3 p.]. Disponible en: http://www.actasdermo.org/es/poroqueratosis-actinica-superficial-diseminada-asociada/articulo/13058578/

6. Pedrozo L, Rodríguez Saa S, Cohen Sabban EN, Cabo H. Dermatoscopía de la poroqueratosis actínica superficial diseminada. Dermatol Argent [Internet] 2015 [citado 10 Nov 2017], 21 (1): [aprox. 2 p.]. Disponible en: http://www.dermatolarg.org.ar/index.php/dermatolarg/article/viewFile/1390/788.

7. Trejo Acuña JR, Ramos Garibay A, Maza de Franco A. Poroqueratosis actínica superficial diseminada tratada con terapia fotodinámica. Rev Cent Dermatol Pascua [Internet] 2015 [citado 10 Nov 2017], 24 (1): [aprox. 2 p.]. Disponible en: http://www.medigraphic.com/pdfs/derma/cd-2015/cd151d.pdf

8. Fernández Sánchez C, Galache Osuna C, Hidalgo García Y, Palacio Aller L, Gonzalvo Rodríguez P. Poroqueratosis lineal. Med Cutan Iber Lat Am [Internet] 2015 [citado 10 Nov 2017]; 43 (2): [aprox. 2 p.]. Disponible en: http://www.medigraphic.com/pdfs/cutanea/mc-2015/mc152h.pdf.

9. Saúl LM, Neglia V, Kien MC, Abeldaño A. Poroqueratosis: comunicación de tres casos. Arch Argent Dermatol [Internet] 2016[citado 10 Nov 2017]; 66 (2): [aprox. 2 p.]. Disponible en: http://archivosdermato.org.ar/Uploads/36Saul-Poroqueratosis.pdf.

10. García Vargas Y, Salinas Hojyo RI, Blanco D, Ramírez N. Casuística de Poroqueratosis del Instituto Dermatológico Dominicano y Cirugía de Piel “Dr. Huberto Bogaert Díaz” durante el periodo 2005-2015. Rev Dom Dermatol. [Internet] 2015 [citado 10 Nov 2017]; 42(1) [aprox. 2 p.]. Disponible en: http://revistadominicanadedermatologia.com/wp-content/uploads/2016/07/Volumen_42_No_1_Ene-Jun-2015.pdf.

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Published

2018-03-02

How to Cite

1.
Acosta Rodríguez A, Martinez Navarro J, Fernández López E. Disseminated Superficial Actinic Porokeratosis. Rev Ciencias Médicas [Internet]. 2018 Mar. 2 [cited 2025 Aug. 2];22(2):385-90. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/3426

Issue

Vol. 22 No. 2 (2018)

Section

CASE REPORTS

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