Lofgren's síndrome as a rare form of acute sarcoidosis

Authors

Keywords:

SARCOIDOSIS, GRANULOMATOUS DISEASE, ERYTHEMA NODOSUM, AUTOIMMUNE DISEASES.

Abstract

Introduction: sarcoidosis is a granulomatous and multisystemic disease of unknown etiology defined as an inflammatory response to an environmental antigen in a genetically susceptible person. Löfgren's syndrome is a form of presentation with stereotypical clinical findings manifested as a triad of acute periarthritis, erythema nodosum and hilar adenopathy.

Case report: we report a case with the characteristic findings of this clinical form in which, after the multidisciplinary discussion of the findings found in the physical examination and complementary studies, it was decided to start treatment with glucocorticoids without performing mediastinal lymph node biopsy, an invasive and risky procedure.

Conclusions: the clinical evolution of the patient was favorable and at present he is asymptomatic, without treatment and without evidence of complications or progression towards the chronic form of the disease after three years of evolution.

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Author Biographies

Iraisy Moreno-González, Hospital Municipal “Augusto César Sandino”. Pinar del Río, Cuba.

Especialista de primer grado en MGI y Endocrinología.

Instructor

Maite Cabrera-Gamez, Instituto Nacional de Endocrinología. La Habana, Cuba.

Especialista de segundo grado en Endocrinología.

Profesora e investigadora auxiliar.

Máster en Salud Pública.

Adalberto Fortún-Prieto, Hospital Clínico Quirúrgico Docente León Cuervo Rubio

Especialista de primer y segundo grado en Medicina Interna.

Especialista de 2do grado en Hematología.

Profesor auxiliar y consultante.

Investigador Auxiliar.

Master en longevidad satisfactoria y educación médica

Oderkys Pineda-Daniel, Hospital Municipal “Augusto César Sandino”. Pinar del Río, Cuba.

Especialista de primer grado en MGI y Nefrología. Profesor Asistende.

Jefe del servicio de Nefrología del Hospital Augusto César Sandino

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Published

2023-06-22

How to Cite

1.
Moreno-González I, Cabrera-Gamez M, Fortún-Prieto A, Pineda-Daniel O. Lofgren’s síndrome as a rare form of acute sarcoidosis. Rev Ciencias Médicas [Internet]. 2023 Jun. 22 [cited 2025 Sep. 19];27:e5521. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/5521