Post anoxic myoclonic encephalopathy or Lance-Adams syndrome

Authors

  • Antonio Javier Garcia Medina Hospital Clinico Quirurgico León Cuervo Rubio

Keywords:

Myoclonic epilepsies, Cerebellar ataxia.

Abstract

Introduction: post anoxic myoclonic encephalopathy or Lance-Adams syndrome was described in 1963, it is a very rare complication that can appear in patients who have suffered from hypoxic episodes or prolonged hypotension, already recovered. They are characterized by myoclonus actions and cerebellar ataxia.

Case report: a patient suffering from two cardiorespiratory arrests, severe-generalized myoclonus of actions appearing after the recovery, which increases with tactile, auditory or nociceptive stimuli, relieving only during sleep, with a clear and progressive deterioration of the general status.  

Conclusion: a successful recovery was observed within the 24 hours of treatment commencing with 4 milligrams of Clonazepam, being asymptomatic and monitored at one, three, six and 12 months.

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Author Biography

Antonio Javier Garcia Medina, Hospital Clinico Quirurgico León Cuervo Rubio

Especialista de Segundo Grado en Neurologia. Profesor Auxiliar, Máster en Longevidad Satisfactoria. Jefe del Grupo Provincial de Neurologia de Pinar del Rio. Jefe del Departamento de Neurologia Hospital CQD LCR

References

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Published

2016-03-18

How to Cite

1.
Garcia Medina AJ. Post anoxic myoclonic encephalopathy or Lance-Adams syndrome. Rev Ciencias Médicas [Internet]. 2016 Mar. 18 [cited 2025 Aug. 21];20(1):152-5. Available from: https://revcmpinar.sld.cu/index.php/publicaciones/article/view/2559

Issue

Vol. 20 No. 1 (2016)

Section

CASE REPORTS

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